Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Broad Center for Mendelian Genomics, |
RCV004586511 | SCV005077903 | uncertain significance | Iron-refractory iron deficiency anemia | 2024-06-19 | criteria provided, single submitter | curation | The heterozygous p.Leu302Gly variant in TOX was identified by our study in 1 individual with IRIDA and restless legs syndrome that is responsive to iron. While this gene is still lacking sufficient evidence to establish a gene-disease relationship, we believe this is a possible novel gene candidate for iron responsive disorders. Given the limited information about this gene-disease relationship, the significance of the p.Leu302Gly variant is uncertain. If you have any additional information about functional evidence or other individuals with this phenotype that also have variants in TOX we encourage you to reach out to us. |