Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV000413102 | SCV000491626 | pathogenic | not provided | 2023-10-25 | criteria provided, single submitter | clinical testing | Nonsense variant predicted to result in protein truncation or nonsense mediated decay in a gene for which loss of function is a known mechanism of disease; Not observed at significant frequency in large population cohorts (gnomAD) |
Juno Genomics, |
RCV004796169 | SCV005417497 | pathogenic | Mowat-Wilson syndrome | criteria provided, single submitter | clinical testing | PM2_Supporting+PVS1+PM6_Supporting |