Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV001267231 | SCV001445412 | pathogenic | Inborn genetic diseases | 2021-03-23 | criteria provided, single submitter | clinical testing | The c.232C>T (p.Q78*) alteration, located in exon 3 (coding exon 2) of the WASHC5 gene, results from a C to T substitution at nucleotide position 232. This changes the amino acid from a glutamine (Q) to a stop codon at amino acid position 78. This alteration is expected to result in loss of function by premature protein truncation or nonsense-mediated mRNA decay. This variant was not reported in population-based cohorts in the Genome Aggregation Database (gnomAD). Based on the available evidence, this alteration is classified as pathogenic. |
Department of Pediatrics, |
RCV004556081 | SCV005045317 | pathogenic | Ritscher-Schinzel syndrome 1 | 2024-02-01 | no assertion criteria provided | clinical testing |