Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Neuberg Centre For Genomic Medicine, |
RCV005208328 | SCV005849321 | uncertain significance | Intellectual disability, X-linked, syndromic, Houge type | criteria provided, single submitter | clinical testing | The observed missense variant c.2388C>G(p.Asp796Glu) in CNKSR2 gene has not been reported previously as a pathogenic variant nor as a benign variant, to our knowledge. This variant is absent in gnomAD Exomes. The amino acid Asp at position 796 is changed to a Glu changing protein sequence and it might alter its composition and physico-chemical properties. Multiple lines of computational evidence (Polyphen-Benign, SIFT-Tolerated and MutationTaster-Polymorphism) predict no damaging effect on protein structure and function for this variant. The reference amino acid p.Asp796Glu in CNKSR2 is predicted as conserved by GERP++ and PhyloP across 100 vertebrates. For these reasons, this variant has been classified as Uncertain Significance. |