Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000461473 | SCV000548906 | pathogenic | Hereditary spastic paraplegia 4 | 2016-10-01 | criteria provided, single submitter | clinical testing | For these reasons, this variant has been classified as Pathogenic. Truncating sequence changes in SPAST are known to be pathogenic (PMID:20932283). This variant has been reported in a family affected with autosomal dominant hereditary spastic paraplegia (AD-HSP)  (PMID: 17916079). This sequence change creates a premature translational stop signal at codon 43 (p.Glu43*) of the SPAST gene. It is expected to result in an absent or disrupted protein product. |