Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
DASA | RCV002308500 | SCV002600249 | likely pathogenic | Fleck corneal dystrophy | 2022-11-03 | criteria provided, single submitter | clinical testing | The c.904C>T;p.(Arg302*) variant creates a premature translational stop signal in the PIKFYVE gene. It is expected to result in an absent or disrupted protein product - PVS1. The variant is present at low allele frequencies population databases (rs1195336213 – gnomAD 0.00006574%; ABraOM no frequency - https://abraom.ib.usp.br/) - PM2_supporting. In summary, the currently available evidence indicates that the variant is likely pathogenic. |