Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Genomics Facility, |
RCV001172378 | SCV001146851 | pathogenic | Immunodeficiency with T and B cell lymphopenia | 2019-12-01 | criteria provided, single submitter | research | Ten patients from seven unrelated pedigrees with variable T and B cell lymphopenia, who are homozygous for six distinct mutations in FCHO1. |
Genomics Facility, |
RCV001194473 | SCV001146888 | pathogenic | Severe congenital neutropenia | 2019-12-01 | no assertion criteria provided | research |