Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
New York Genome Center | RCV001839172 | SCV002099110 | uncertain significance | Developmental and epileptic encephalopathy, 64 | 2021-04-09 | criteria provided, single submitter | clinical testing | The c.1488del, p.Gly497AlafsTer6, frameshift variant in the RHOBTB2 gene has not been reported in the literature. This variant is not reported in the gnomAD v3 database, indicating this is a rare allele. The variant is expected to result in a truncated protein or protein loss due to nonsense-mediated messenger decay (NMD). The current clinical and genetic evidence is not sufficient to establish whether loss-of-function variants in RHOBTB2 gene cause disease. Based on the available evidence, the variant c.1488del, p.Gly497AlafsTer6, in the RHOBTB2 gene is classified as a Variant of Uncertain Significance. |