Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ce |
RCV000999025 | SCV001155410 | uncertain significance | not provided | 2018-06-01 | criteria provided, single submitter | clinical testing | |
Gene |
RCV000999025 | SCV001793381 | pathogenic | not provided | 2023-05-11 | criteria provided, single submitter | clinical testing | Nonsense variant predicted to result in protein truncation or nonsense mediated decay in a gene for which loss-of-function is a known mechanism of disease; Has not been previously published as pathogenic or benign to our knowledge |
Labcorp Genetics |
RCV001858893 | SCV002230686 | pathogenic | Hereditary spastic paraplegia 54 | 2022-07-06 | criteria provided, single submitter | clinical testing | For these reasons, this variant has been classified as Pathogenic. Algorithms developed to predict the effect of sequence changes on RNA splicing suggest that this variant may disrupt the consensus splice site. ClinVar contains an entry for this variant (Variation ID: 810276). This variant has not been reported in the literature in individuals affected with DDHD2-related conditions. This variant is present in population databases (rs377293194, gnomAD 0.009%). This sequence change creates a premature translational stop signal (p.Arg190*) in the DDHD2 gene. It is expected to result in an absent or disrupted protein product. Loss-of-function variants in DDHD2 are known to be pathogenic (PMID: 23176823, 23486545). |