Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Prevention |
RCV004550647 | SCV004112506 | pathogenic | CAMTA1-related disorder | 2023-01-30 | criteria provided, single submitter | clinical testing | The CAMTA1 c.2685_2686dupGC variant is predicted to result in a frameshift and premature protein termination (p.Gln896Argfs*21). To our knowledge, this variant has not been reported in the literature or in a large population database (http://gnomad.broadinstitute.org), indicating this variant is rare. This variant has been observed de novo in an individual with features consistent with CAMTA1-associated disease (Internal Data, PreventionGenetics). Frameshift variants in CAMTA1 are expected to be pathogenic. This variant is interpreted as pathogenic. |