Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001937933 | SCV002183358 | uncertain significance | Familial aplasia of the vermis; Meckel-Gruber syndrome | 2022-06-04 | criteria provided, single submitter | clinical testing | This sequence change creates a premature translational stop signal (p.Asp1271Thrfs*24) in the RPGRIP1L gene. While this is not anticipated to result in nonsense mediated decay, it is expected to disrupt the last 45 amino acid(s) of the RPGRIP1L protein. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. ClinVar contains an entry for this variant (Variation ID: 1408000). This variant has not been reported in the literature in individuals affected with RPGRIP1L-related conditions. This variant is present in population databases (rs761954313, gnomAD 0.006%). |
Fulgent Genetics, |
RCV002490244 | SCV002783059 | uncertain significance | Joubert syndrome 7; Meckel syndrome, type 5; COACH syndrome 3 | 2021-12-03 | criteria provided, single submitter | clinical testing |