Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
3billion | RCV003152824 | SCV003841268 | likely pathogenic | Dyschromatosis universalis hereditaria 1 | 2023-02-23 | criteria provided, single submitter | clinical testing | The variant is not observed in the gnomAD v2.1.1 dataset. The variant is located in a mutational hot spot and/or well-established functional domain in which established pathogenic variants have been reported. Missense changes are a common disease-causing mechanism. A different missense change at the same codon (p.Thr525Arg) has been reported to be associated with SASH1 related disorder (PMID: 32981204). Therefore, this variant is classified as Likely pathogenic according to the recommendation of ACMG/AMP guideline. |