Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV000519307 | SCV000621005 | uncertain significance | not provided | 2017-09-28 | criteria provided, single submitter | clinical testing | The A778V variant has not been published as a pathogenic variant, nor has it been reported as a benign variant to our knowledge. The A778V variant is not observed in large population cohorts (Lek et al., 2016). This variant is a conservative amino acid substitution, which is not likely to impact secondary protein structure as these residues share similar properties. This substitution occurs at a position that is not conserved. However, in silico analysis is inconsistent in its predictions as to whether or not the variant is damaging to the protein structure/function. |
Service de Génétique Moléculaire, |
RCV001256984 | SCV001433530 | likely pathogenic | Rare genetic intellectual disability | no assertion criteria provided | clinical testing |