Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Neuberg Centre For Genomic Medicine, |
RCV005208352 | SCV005849357 | uncertain significance | Cardiac anomalies - developmental delay - facial dysmorphism syndrome | 2023-06-22 | criteria provided, single submitter | clinical testing | The observed missense variant c.3278A>G(p.Asn1093Ser) in MED13L gene has not been reported previously as a pathogenic variant nor as a benign variant, to our knowledge. This variant is absent in gnomAD Exomes. The amino acid Asn at position 1093 is changed to a Ser changing protein sequence and it might alter its composition and physico-chemical properties. Computational evidence (Polyphen-Benign, SIFT-Tolerated and MutationTaster-disease causing) predicts conflicting evidence on protein structure and function for this variant.The reference amino acid p.Asn1093Ser in MED13L is predicted as conserved by GERP++ and PhyloP across 100 vertebrates. For these reasons, this variant has been classified as Uncertain Significance. |