Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Institute of Human Genetics, |
RCV000496127 | SCV000586705 | pathogenic | Cardiac anomalies - developmental delay - facial dysmorphism syndrome | 2017-08-01 | criteria provided, single submitter | clinical testing | De novo LOF variant in a patient with moderate ID, attention difficulties, strabismus, hypotonia, cryptorchidism. |
Laboratorio de Genetica e Diagnostico Molecular, |
RCV002252141 | SCV002522836 | pathogenic | See cases | 2021-08-31 | criteria provided, single submitter | clinical testing | ACMG classification criteria: PVS1, PS4, PM2, PM6 |