Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Athena Diagnostics | RCV000517713 | SCV000616319 | uncertain significance | not specified | 2017-04-28 | criteria provided, single submitter | clinical testing | |
Mayo Clinic Laboratories, |
RCV001509471 | SCV001716203 | uncertain significance | not provided | 2021-09-14 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV002525107 | SCV003020651 | uncertain significance | Spastic paraplegia | 2022-08-20 | criteria provided, single submitter | clinical testing | This sequence change replaces arginine, which is basic and polar, with histidine, which is basic and polar, at codon 148 of the ZFYVE26 protein (p.Arg148His). This variant is present in population databases (rs144919978, gnomAD 0.07%). This variant has not been reported in the literature in individuals affected with ZFYVE26-related conditions. ClinVar contains an entry for this variant (Variation ID: 448891). Algorithms developed to predict the effect of missense changes on protein structure and function output the following: SIFT: "Deleterious"; PolyPhen-2: "Benign"; Align-GVGD: "Class C0". The histidine amino acid residue is found in multiple mammalian species, which suggests that this missense change does not adversely affect protein function. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |