Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Baylor Genetics | RCV001330668 | SCV001522417 | uncertain significance | Autosomal recessive cerebellar ataxia-saccadic intrusion syndrome | 2019-11-08 | criteria provided, single submitter | clinical testing | This variant was determined to be of uncertain significance according to ACMG Guidelines, 2015 [PMID:25741868]. |
Labcorp Genetics |
RCV002546404 | SCV003492562 | uncertain significance | not provided | 2022-05-30 | criteria provided, single submitter | clinical testing | In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. Algorithms developed to predict the effect of missense changes on protein structure and function (SIFT, PolyPhen-2, Align-GVGD) all suggest that this variant is likely to be tolerated. ClinVar contains an entry for this variant (Variation ID: 1029396). This variant has not been reported in the literature in individuals affected with VPS13D-related conditions. This variant is present in population databases (no rsID available, gnomAD 0.0009%). This sequence change replaces proline, which is neutral and non-polar, with arginine, which is basic and polar, at codon 2788 of the VPS13D protein (p.Pro2788Arg). |
Ambry Genetics | RCV002546405 | SCV003753249 | uncertain significance | Inborn genetic diseases | 2024-12-10 | criteria provided, single submitter | clinical testing | The c.8363C>G (p.P2788R) alteration is located in exon 38 (coding exon 37) of the VPS13D gene. This alteration results from a C to G substitution at nucleotide position 8363, causing the proline (P) at amino acid position 2788 to be replaced by an arginine (R). Based on insufficient or conflicting evidence, the clinical significance of this alteration remains unclear. |
Breakthrough Genomics, |
RCV002546404 | SCV005186473 | uncertain significance | not provided | criteria provided, single submitter | not provided |