Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV000599429 | SCV000710779 | uncertain significance | not provided | 2018-03-06 | criteria provided, single submitter | clinical testing | A variant of uncertain significance has been identified in the KANSL1 gene. The c.779dupG variant has not been published as a pathogenic variant, nor has it been reported as a benign variant to our knowledge. The c.779dupG variant is observed in 2/30778 (0.01%) alleles from individuals of South Asian background (Lek et al., 2016). The c.779dupG variant causes a frameshift starting with codon Valine 261, changes this amino acid to a Cysteine residue and creates a premature Stop codon at position 6 of the new reading frame, denotedp.Val261CysfsX6. If present in the primary transcript, this variant is predicted to cause loss of normal protein function either through protein truncation or nonsense-mediated mRNA decay. Based on the currently available information, it is unclear whether this variant is a pathogenic variant or a rare benign variant. |