Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Counsyl | RCV000673433 | SCV000798634 | uncertain significance | Cobalamin C disease | 2018-03-16 | criteria provided, single submitter | clinical testing | |
Baylor Genetics | RCV000673433 | SCV001527837 | uncertain significance | Cobalamin C disease | 2018-04-18 | criteria provided, single submitter | clinical testing | This variant was determined to be of uncertain significance according to ACMG Guidelines, 2015 [PMID:25741868]. |
Gene |
RCV001771922 | SCV001992398 | uncertain significance | not provided | 2021-01-18 | criteria provided, single submitter | clinical testing | Not observed at a significant frequency in large population cohorts (Lek et al., 2016); Frameshift variant predicted to result in protein truncation as the last 16 amino acids are lost and replaced with 42 incorrect amino acids, although loss-of-function variants have not been reported downstream of this position in the protein; Has not been previously published as pathogenic or benign to our knowledge |
Genome- |
RCV000673433 | SCV004178234 | uncertain significance | Cobalamin C disease | 2023-04-11 | criteria provided, single submitter | clinical testing |