Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Molecular Genetics Laboratory, |
RCV004795259 | SCV005415404 | likely pathogenic | Autism spectrum disorder due to AUTS2 deficiency | 2024-11-27 | criteria provided, single submitter | clinical testing | This variant was detected in a female with moderate moderate intellectual disability, microcephaly, delayed speech and language development. Rare splicing variants affecting the AUTS2 gene are documented as a molecular cause of "autosomal dominant intellectual developmental disorder 26" (MRD26, OMIM:615834) (PMID:27075013;25205402;23332918). There is a different splicing variant c.1214+1G>A in the LOVD database, classified as pathogenic/likely pathogenic (DB-ID: AUTS2_000154). To conclude, the variant is classified as likely pathogenic (ACMG PVS1, PM2). |