Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Institute of Medical Genetics and Applied Genomics, |
RCV001682650 | SCV001905542 | pathogenic | not provided | 2021-09-15 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV001682650 | SCV002194551 | pathogenic | not provided | 2022-09-04 | criteria provided, single submitter | clinical testing | This sequence change creates a premature translational stop signal (p.Lys120Glufs*4) in the PRPF31 gene. It is expected to result in an absent or disrupted protein product. Loss-of-function variants in PRPF31 are known to be pathogenic (PMID: 18317597, 23950152). This variant is not present in population databases (gnomAD no frequency). This premature translational stop signal has been observed in individual(s) with retinitis pigmentosa (PMID: 32100970). ClinVar contains an entry for this variant (Variation ID: 1275773). For these reasons, this variant has been classified as Pathogenic. |