Total submissions: 7
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001054271 | SCV001218576 | likely benign | Short-rib thoracic dysplasia 10 with or without polydactyly; Retinitis pigmentosa 71 | 2024-12-18 | criteria provided, single submitter | clinical testing | |
Gene |
RCV002291713 | SCV002584499 | uncertain significance | not provided | 2023-04-12 | criteria provided, single submitter | clinical testing | In silico analysis supports that this missense variant has a deleterious effect on protein structure/function; Has not been previously published as pathogenic or benign to our knowledge |
New York Genome Center | RCV002468131 | SCV002764515 | uncertain significance | Short-rib thoracic dysplasia 10 with or without polydactyly; Retinitis pigmentosa 71; Bardet-Biedl syndrome 20 | 2022-01-14 | criteria provided, single submitter | clinical testing | |
Fulgent Genetics, |
RCV002468131 | SCV002797706 | uncertain significance | Short-rib thoracic dysplasia 10 with or without polydactyly; Retinitis pigmentosa 71; Bardet-Biedl syndrome 20 | 2024-03-29 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV002553339 | SCV003541922 | uncertain significance | Inborn genetic diseases | 2021-08-13 | criteria provided, single submitter | clinical testing | The c.1313C>T (p.P438L) alteration is located in exon 13 (coding exon 13) of the IFT172 gene. This alteration results from a C to T substitution at nucleotide position 1313, causing the proline (P) at amino acid position 438 to be replaced by a leucine (L). Based on insufficient or conflicting evidence, the clinical significance of this alteration remains unclear. |
Genetic Services Laboratory, |
RCV003151274 | SCV003839599 | uncertain significance | not specified | 2022-07-20 | no assertion criteria provided | clinical testing | DNA sequence analysis of the IFT172 gene demonstrated a sequence change, c.1313C>T, in exon 13 that results in an amino acid change, p.Pro438Leu. This sequence change has been described in the gnomAD database with a frequency of 0.096% in the African/African American subpopulation (dbSNP rs367930028). The p.Pro438Leu change affects a highly conserved amino acid residue located in a domain of the IFT172 protein that is known to be functional. In-silico pathogenicity prediction tools (SIFT, PolyPhen2, Align GVGD, REVEL) provide contradictory results for the p.Pro438Leu substitution. This sequence change does not appear to have been previously described in individuals with IFT172-related disorders. Due to insufficient evidences and the lack of functional studies, the clinical significance of the p.Pro438Leu change remains unknown at this time. |
Prevention |
RCV004553596 | SCV004106084 | uncertain significance | IFT172-related disorder | 2024-03-01 | no assertion criteria provided | clinical testing | The IFT172 c.1313C>T variant is predicted to result in the amino acid substitution p.Pro438Leu. To our knowledge, this variant has not been reported in the literature. This variant is reported in 0.096% of alleles in individuals of African descent in gnomAD. Although we suspect that this variant may be benign, at this time, the clinical significance of this variant is uncertain due to the absence of conclusive functional and genetic evidence. |