Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Institute for Human Genetics and Genomic Medicine, |
RCV001290431 | SCV001478460 | uncertain significance | Short-rib thoracic dysplasia 10 with or without polydactyly | 2021-02-09 | criteria provided, single submitter | clinical testing | The variant (rs1045778698) is listed in gnomAD with a frequency of 0.021% (60/282274) (02/05/2021). In bioinformatics, the change is classified as "probably disease causing" (CADDPhred 25.8, MutationTaster). The variant is currently classified as a "variant of uncertain clinical significance" (ACMG criteria). |
Fulgent Genetics, |
RCV005029859 | SCV005651398 | uncertain significance | Short-rib thoracic dysplasia 10 with or without polydactyly; Retinitis pigmentosa 71; Bardet-Biedl syndrome 20 | 2023-12-27 | criteria provided, single submitter | clinical testing |