Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Fulgent Genetics, |
RCV002505011 | SCV002813897 | pathogenic | Short-rib thoracic dysplasia 10 with or without polydactyly; Retinitis pigmentosa 71; Bardet-Biedl syndrome 20 | 2024-05-25 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV002514456 | SCV003524157 | pathogenic | Short-rib thoracic dysplasia 10 with or without polydactyly; Retinitis pigmentosa 71 | 2024-12-04 | criteria provided, single submitter | clinical testing | This sequence change creates a premature translational stop signal (p.Arg1642Lysfs*32) in the IFT172 gene. It is expected to result in an absent or disrupted protein product. Loss-of-function variants in IFT172 are known to be pathogenic (PMID: 24140113). This variant is present in population databases (rs587777078, gnomAD 0.01%). This premature translational stop signal has been observed in individual(s) with Mainzer-Saldino syndrome (PMID: 24140113). For these reasons, this variant has been classified as Pathogenic. |
OMIM | RCV000083269 | SCV000115349 | pathogenic | Short-rib thoracic dysplasia 10 without polydactyly | 2013-11-07 | no assertion criteria provided | literature only |