Total submissions: 6
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Invitae | RCV001303423 | SCV001492669 | likely benign | Short-rib thoracic dysplasia 10 with or without polydactyly; Retinitis pigmentosa 71 | 2023-12-22 | criteria provided, single submitter | clinical testing | |
Fulgent Genetics, |
RCV002490732 | SCV002790546 | uncertain significance | Short-rib thoracic dysplasia 10 with or without polydactyly; Retinitis pigmentosa 71; Bardet-Biedl syndrome 20 | 2022-05-19 | criteria provided, single submitter | clinical testing | |
Gene |
RCV003153361 | SCV003842729 | uncertain significance | not provided | 2022-09-15 | criteria provided, single submitter | clinical testing | In silico analysis supports that this missense variant has a deleterious effect on protein structure/function; This variant is associated with the following publications: (PMID: 24140113, 28118382) |
Ambry Genetics | RCV003278664 | SCV003955753 | uncertain significance | Inborn genetic diseases | 2023-03-24 | criteria provided, single submitter | clinical testing | The c.886C>T (p.R296W) alteration is located in exon 9 (coding exon 9) of the IFT172 gene. This alteration results from a C to T substitution at nucleotide position 886, causing the arginine (R) at amino acid position 296 to be replaced by a tryptophan (W). Based on insufficient or conflicting evidence, the clinical significance of this alteration remains unclear. |
Prevention |
RCV004549522 | SCV004106372 | uncertain significance | IFT172-related disorder | 2024-02-16 | criteria provided, single submitter | clinical testing | The IFT172 c.886C>T variant is predicted to result in the amino acid substitution p.Arg296Trp. This variant was reported in the homozygous state in an individual with Mainzer-Saldino syndrome; however, no additional functional or familial segregation studies confirmed the pathogenicity of this change (Halbritter et al. 2013. PubMed ID: 24140113). This variant has an allele frequency up to ~0.1% in some populations, which is higher than expected for a fully penetrant IFT172 variant. At this time, the clinical significance of this variant is uncertain due to the absence of conclusive functional and genetic evidence. |
OMIM | RCV000083274 | SCV000115354 | pathogenic | Short-rib thoracic dysplasia 10 without polydactyly | 2013-11-07 | no assertion criteria provided | literature only |