Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Victorian Clinical Genetics Services, |
RCV002472123 | SCV002768542 | uncertain significance | Early-onset progressive encephalopathy-hearing loss-pons hypoplasia-brain atrophy syndrome | 2019-08-28 | criteria provided, single submitter | clinical testing | A heterozygous missense variant was identified, NM_016030.5(TRAPPC12):c.361G>A in exon 2 of 12 of the TRAPPC12 gene. This substitution is predicted to create a minor amino acid change from glutamic acid to lysine at position 121 of the protein, NP_057114.5(TRAPPC12):p.(Glu121Lys). The glutamic acid at this position is only present, but also conserved, in mammals (100 vertebrates, UCSC), but is not situated in a known functional domain. In silico software predicts this variant to be benign (Polyphen, SIFT, CADD, Mutation Taster). The variant is present in the gnomAD population database at a frequency of 0.13% (132 heterozygotes, 1 homozygote). The variant has not been previously reported in a clinical testing setting. Based on information available at the time of curation, this variant has been classified as a VARIANT of UNCERTAIN SIGNIFICANCE (VUS) with LOW CLINICAL RELEVANCE. |
Labcorp Genetics |
RCV003669323 | SCV004391303 | benign | not provided | 2024-11-27 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV004067597 | SCV004971936 | likely benign | Inborn genetic diseases | 2024-01-09 | criteria provided, single submitter | clinical testing | This alteration is classified as likely benign based on a combination of the following: seen in unaffected individuals, population frequency, intact protein function, lack of segregation with disease, co-occurrence, RNA analysis, in silico models, amino acid conservation, lack of disease association in case-control studies, and/or the mechanism of disease or impacted region is inconsistent with a known cause of pathogenicity. |
Prevention |
RCV003896205 | SCV004718699 | benign | TRAPPC12-related disorder | 2019-09-11 | no assertion criteria provided | clinical testing | This variant is classified as benign based on ACMG/AMP sequence variant interpretation guidelines (Richards et al. 2015 PMID: 25741868, with internal and published modifications). |