Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
SIB Swiss Institute of Bioinformatics | RCV000003349 | SCV000787508 | uncertain significance | Shwachman-Diamond syndrome 1 | 2018-04-16 | criteria provided, single submitter | curation | This variant is interpreted as a Uncertain Significance, for Shwachman-Diamond syndrome, Autosomal Recessive inheritance. The following ACMG Tag(s) were applied: PM2 => Absent from controls (or at extremely low frequency if recessive) in Exome Sequencing Project, 1000 Genomes Project, or Exome Aggregation Consortium. PP3 => Multiple lines of computational evidence support a deleterious effect on the gene or gene product. |
OMIM | RCV000003349 | SCV000023507 | pathogenic | Shwachman-Diamond syndrome 1 | 2003-01-01 | no assertion criteria provided | literature only |