Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Prevention |
RCV003398425 | SCV004105452 | likely pathogenic | SAR1B-related disorder | 2023-07-24 | criteria provided, single submitter | clinical testing | The SAR1B c.537T>A variant is predicted to result in the amino acid substitution p.Ser179Arg. This variant was reported as pathogenic in patients with chylomicron retention disease (Jones et al. 2003. PubMed ID: 12692552; Charcosset et al. 2007. PubMed ID: 17945526). This variant is reported in 0.0044% of alleles in individuals of European (Non-Finnish) descent in gnomAD (http://gnomad.broadinstitute.org/variant/5-133942700-A-T). This variant is interpreted as likely pathogenic. |
OMIM | RCV000003059 | SCV000023217 | pathogenic | Chylomicron retention disease | 2008-01-01 | no assertion criteria provided | literature only | |
Gene |
RCV000003059 | SCV002318919 | not provided | Chylomicron retention disease | no assertion provided | literature only |