Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Institute of Human Genetics, |
RCV003226893 | SCV003922062 | likely pathogenic | Basal cell nevus syndrome 2 | 2023-05-05 | criteria provided, single submitter | clinical testing | The variant c.946_952del (p.(Leu316Serfs*43)) in exon 8 of the SUFU gene is not found in the gnomAD database and it creates a frame shift starting at codon Leu316. The new reading frame ends in a STOP codon at position 43. Truncating variants in the SUFU gene are a known mechanism of disease. ACMG criteria used for classification: PVS1, PM2. |