Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Women's Health and Genetics/Laboratory Corporation of America, |
RCV004689540 | SCV005185813 | pathogenic | Oculocutaneous albinism type 4 | 2024-05-15 | criteria provided, single submitter | clinical testing | Variant summary: SLC45A2 c.1456G>A (p.Ala486Thr) results in a non-conservative amino acid change in the encoded protein sequence. Five of five in-silico tools predict a damaging effect of the variant on protein function. The variant was absent in 251166 control chromosomes. c.1456G>A has been reported in the literature in multiple individuals affected with albinism (example, Wei_2022). These data indicate that the variant is very likely to be associated with disease. To our knowledge, no experimental evidence demonstrating an impact on protein function has been reported. The following publication has been ascertained in the context of this evaluation (PMID: 34838614). No submitters have cited clinical-significance assessments for this variant to ClinVar. Based on the evidence outlined above, the variant was classified as pathogenic. |
Juno Genomics, |
RCV004796878 | SCV005418838 | likely pathogenic | SKIN/HAIR/EYE PIGMENTATION 5, BLACK/NONBLACK HAIR; Oculocutaneous albinism type 4 | criteria provided, single submitter | clinical testing | PM2_Supporting+PP3_Moderate+PM5_Supporting+PM3_Supporting+PP4 | |
Fulgent Genetics, |
RCV004796878 | SCV005671152 | pathogenic | SKIN/HAIR/EYE PIGMENTATION 5, BLACK/NONBLACK HAIR; Oculocutaneous albinism type 4 | 2024-05-24 | criteria provided, single submitter | clinical testing | |
Prevention |
RCV004756575 | SCV005363171 | likely pathogenic | SLC45A2-related disorder | 2024-08-19 | no assertion criteria provided | clinical testing | The SLC45A2 c.1456G>A variant is predicted to result in the amino acid substitution p.Ala486Thr. This variant has been reported in multiple individuals with oculocutaneous albinism (Xue et al. 2016. PubMed ID: 27706749; Chuan et al. 2021. PubMed ID: 32552135 Wei. 2022. PubMed ID: 34838614). This variant has not been reported in a large population database, indicating this variant is rare. Given the evidence, we interpret this variant as likely pathogenic. |