Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV002968016 | SCV003287776 | pathogenic | not provided | 2024-07-29 | criteria provided, single submitter | clinical testing | This sequence change affects the initiator methionine of the SLC45A2 mRNA. The next in-frame methionine is located at codon 37. This variant is present in population databases (rs764544992, gnomAD 0.003%). Disruption of the initiator codon has been observed in individual(s) with oculocutaneous albinism (Invitae). In at least one individual the data is consistent with being in trans (on the opposite chromosome) from a pathogenic variant. ClinVar contains an entry for this variant (Variation ID: 2075883). For these reasons, this variant has been classified as Pathogenic. |
Fulgent Genetics, |
RCV005034541 | SCV005671176 | likely pathogenic | SKIN/HAIR/EYE PIGMENTATION 5, BLACK/NONBLACK HAIR; Oculocutaneous albinism type 4 | 2024-06-13 | criteria provided, single submitter | clinical testing |