Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Laboratory for Molecular Medicine, |
RCV000151394 | SCV000199402 | pathogenic | Rare genetic deafness | 2014-10-17 | criteria provided, single submitter | clinical testing | The c.5531+1G>A variant in MYO15A has not been previously reported in individual s with hearing loss and was absent from large population studies. This variant o ccurs in the invariant region (+ 1/2) of the 5' splice site consensus sequence a nd is predicted to cause altered splicing leading to an abnormal or absent prote in. In summary, this variant meets our criteria to be classified as pathogenic f or sensorineural hearing loss in an autosomal recessive manner (www.partners.org /personalizedmedicine/LMM). |
Molecular Diagnosis Center for Deafness | RCV001254925 | SCV001332617 | pathogenic | Autosomal recessive nonsyndromic hearing loss 3 | 2020-02-27 | criteria provided, single submitter | case-control |