Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Hereditary Hearing Loss Research Unit, |
RCV001250120 | SCV001366122 | pathogenic | Autosomal recessive nonsyndromic hearing loss 3 | criteria provided, single submitter | case-control | The variant p.Y1981X was observed along with another MYO15A variant p.L1485P, in compound heterozygous state, in the affected individuals. Hence, reporting this heterozygous variant in Autosomal recessive Hearing Loss. | |
Labcorp Genetics |
RCV003574862 | SCV004337680 | pathogenic | not provided | 2024-01-04 | criteria provided, single submitter | clinical testing | This sequence change creates a premature translational stop signal (p.Tyr1891*) in the MYO15A gene. It is expected to result in an absent or disrupted protein product. Loss-of-function variants in MYO15A are known to be pathogenic (PMID: 17546645). This variant is not present in population databases (gnomAD no frequency). This premature translational stop signal has been observed in individual(s) with deafness (PMID: 34374074). ClinVar contains an entry for this variant (Variation ID: 973491). For these reasons, this variant has been classified as Pathogenic. |