Total submissions: 8
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Laboratory for Molecular Medicine, |
RCV000038978 | SCV000062656 | benign | not specified | 2012-12-19 | criteria provided, single submitter | clinical testing | Thr2205Ile variant in exon 31 of MYO15A: This variant is not expected to have cl inical significance because it has been identified in has been reported in 0.4% (33/8348) of European American chromosomes chromosomes from a broad population b y the NHLBI Exome Sequencing Project (http://evs.gs.washington.edu/EVS/; dbSNP r s121908970). It has been reported in the hemizygous state in an individual with Smith-Lemli-Opitz sydnrome (Liburd 2001) and homozygous in one individual with hearing loss who also carries a homozygous nonsense variant in MYO15A (Nal 2007) ; however, these reports are likely due to the frequency of this variant and not a reflection of its role in hearing loss. |
Eurofins Ntd Llc |
RCV000038978 | SCV000340324 | benign | not specified | 2016-03-21 | criteria provided, single submitter | clinical testing | |
Gene |
RCV000835662 | SCV000977464 | benign | not provided | 2019-04-23 | criteria provided, single submitter | clinical testing | This variant is associated with the following publications: (PMID: 30245029, 11735029, 17546645, 12545186, 23208854, 26308726, 27375115, 30579064) |
Invitae | RCV000835662 | SCV001023231 | benign | not provided | 2024-01-31 | criteria provided, single submitter | clinical testing | |
Illumina Laboratory Services, |
RCV001122993 | SCV001281785 | uncertain significance | Autosomal recessive nonsyndromic hearing loss 3 | 2017-04-27 | criteria provided, single submitter | clinical testing | This variant was observed as part of a predisposition screen in an ostensibly healthy population. A literature search was performed for the gene, cDNA change, and amino acid change (where applicable). Publications were found based on this search. However, the evidence from the literature, in combination with allele frequency data from public databases where available, was not sufficient to rule this variant in or out of causing disease. Therefore, this variant is classified as a variant of unknown significance. |
Ce |
RCV000835662 | SCV001334834 | likely benign | not provided | 2020-03-01 | criteria provided, single submitter | clinical testing | |
Molecular Genetics, |
RCV003993739 | SCV004812531 | likely benign | Nonsyndromic genetic hearing loss | 2024-01-05 | criteria provided, single submitter | clinical testing | Based on the classification scheme RMH Modified ACMG/AMP Guidelines v1.6.1, this variant is classified as Likely benign. Following criteria are met: BS1 - BS1: Allele frequency is greater than expected for disorder PP3 - PP3: Computational evidence support a deleterious effect on the gene or gene product (REVEL >=0.644 & <0.932 OR SpliceAI >0.50) |
OMIM | RCV000007371 | SCV000027570 | pathogenic | Deafness, with smith-magenis syndrome | 2001-11-01 | no assertion criteria provided | literature only |