Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
3billion | RCV002251184 | SCV002521675 | uncertain significance | Autosomal recessive nonsyndromic hearing loss 3 | 2022-05-22 | criteria provided, single submitter | clinical testing | The variant was co-segregated with Deafness, autosomal recessive 3 in multiple affected family members (PMID: 25792667). In silico prediction tools and conservation analysis predicted that this variant was probably damaging to the protein structure/function (REVEL: 0.936>=0.6, SPLICEAI: 0.73). . It is absent from the gnomAD v2.1.1 dataset. Amino acid change identical to known pathogenic variant has been previously reported with supporting evidence; this might be considered evidence of a supporting level (PMID:25792667). Therefore, this variant is classified as uncertain significanceaccording to the recommendation of ACMG/AMP guideline. |