Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Columbia University Laboratory of Personalized Genomic Medicine, |
RCV004586460 | SCV005073684 | likely pathogenic | Neurodevelopmental disorder | 2024-07-05 | criteria provided, single submitter | clinical testing | Based on ACMG Variant Interpretation Guidelines: PS3, PM2, PM3, PP3 |
Institute of Human Genetics, |
RCV004759425 | SCV005368446 | uncertain significance | SPOUT1-associated neurodevelopmental disorder | 2024-07-24 | criteria provided, single submitter | clinical testing | This variant was identified as homozygous. Two affected brothers, consanguinous parents |
OMIM | RCV005254921 | SCV005907137 | pathogenic | NEURODEVELOPMENTAL DISORDER WITH POOR GROWTH, SEIZURES, AND BRAIN ABNORMALITIES | 2025-04-07 | no assertion criteria provided | literature only |