Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV004127850 | SCV003604332 | uncertain significance | not specified | 2022-05-18 | criteria provided, single submitter | clinical testing | The c.584G>A (p.R195H) alteration is located in exon 6 (coding exon 5) of the SPTBN5 gene. This alteration results from a G to A substitution at nucleotide position 584, causing the arginine (R) at amino acid position 195 to be replaced by a histidine (H). Based on insufficient or conflicting evidence, the clinical significance of this alteration remains unclear. |
Ce |
RCV003404163 | SCV004136413 | benign | not provided | 2022-07-01 | criteria provided, single submitter | clinical testing | SPTBN5: BS1, BS2 |
Prevention |
RCV003963742 | SCV004784918 | likely benign | SPTBN5-related disorder | 2023-03-20 | no assertion criteria provided | clinical testing | This variant is classified as likely benign based on ACMG/AMP sequence variant interpretation guidelines (Richards et al. 2015 PMID: 25741868, with internal and published modifications). |