Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Revvity Omics, |
RCV001783594 | SCV002017098 | pathogenic | Microcephalic primordial dwarfism, Alazami type | 2019-10-03 | criteria provided, single submitter | clinical testing | |
3billion | RCV001783594 | SCV004013615 | uncertain significance | Microcephalic primordial dwarfism, Alazami type | criteria provided, single submitter | clinical testing | The variant is not observed in the gnomAD v2.1.1 dataset. Inframe deletion located in a nonrepeat region: predicted to change the length of the protein and disrupt normal protein function. The variant has been reported to be associated with LARP7 related disorder (ClinVar ID: VCV001323230). However, the evidence of pathogenicity is insufficient at this time. Therefore, this variant is classified as Uncertain significance according to the recommendation of ACMG/AMP guideline. |