Total submissions: 5
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000794881 | SCV000934315 | uncertain significance | Myopathy, proximal, and ophthalmoplegia | 2025-01-12 | criteria provided, single submitter | clinical testing | This sequence change replaces arginine, which is basic and polar, with histidine, which is basic and polar, at codon 1481 of the MYH2 protein (p.Arg1481His). This variant is present in population databases (rs199751037, gnomAD 0.04%). This variant has not been reported in the literature in individuals affected with MYH2-related conditions. ClinVar contains an entry for this variant (Variation ID: 641606). Invitae Evidence Modeling of protein sequence and biophysical properties (such as structural, functional, and spatial information, amino acid conservation, physicochemical variation, residue mobility, and thermodynamic stability) indicates that this missense variant is expected to disrupt MYH2 protein function with a positive predictive value of 80%. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |
Ambry Genetics | RCV002535913 | SCV003710809 | uncertain significance | Inborn genetic diseases | 2022-08-08 | criteria provided, single submitter | clinical testing | The c.4442G>A (p.R1481H) alteration is located in exon 32 (coding exon 30) of the MYH2 gene. This alteration results from a G to A substitution at nucleotide position 4442, causing the arginine (R) at amino acid position 1481 to be replaced by a histidine (H). Based on insufficient or conflicting evidence, the clinical significance of this alteration remains unclear. |
Revvity Omics, |
RCV000794881 | SCV003809471 | uncertain significance | Myopathy, proximal, and ophthalmoplegia | 2023-12-01 | criteria provided, single submitter | clinical testing | |
Human Genetics Bochum, |
RCV000794881 | SCV004704491 | uncertain significance | Myopathy, proximal, and ophthalmoplegia | 2023-04-18 | criteria provided, single submitter | clinical testing | ACMG criteria used to clasify this variant: PP3_MOD |
Gene |
RCV004789194 | SCV005401540 | uncertain significance | not provided | 2024-05-12 | criteria provided, single submitter | clinical testing | In silico analysis supports that this missense variant has a deleterious effect on protein structure/function; Has not been previously published as pathogenic or benign to our knowledge |