Total submissions: 5
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Chan Lab, |
RCV000156942 | SCV000206663 | likely pathogenic | Delayed puberty | 2014-11-01 | criteria provided, single submitter | case-control | |
Mendelics | RCV000987280 | SCV001136537 | uncertain significance | Cerebral arteriovenous malformation | 2019-05-28 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV001850174 | SCV002129240 | uncertain significance | not provided | 2021-09-26 | criteria provided, single submitter | clinical testing | This sequence change replaces proline with leucine at codon 191 of the IL17RD protein (p.Pro191Leu). The proline residue is highly conserved and there is a moderate physicochemical difference between proline and leucine. This variant is present in population databases (rs200088377, ExAC 0.1%). This variant has been observed in individual(s) with idiopathic hypogonadotropic hypogonadism (PMID: 32389901). ClinVar contains an entry for this variant (Variation ID: 180145). Algorithms developed to predict the effect of missense changes on protein structure and function are either unavailable or do not agree on the potential impact of this missense change (SIFT: "Not Available"; PolyPhen-2: "Possibly Damaging"; Align-GVGD: "Not Available"). In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |
Ce |
RCV001850174 | SCV004150362 | benign | not provided | 2022-05-01 | criteria provided, single submitter | clinical testing | IL17RD: BS1, BS2 |
Genetic Services Laboratory, |
RCV003150956 | SCV003839606 | uncertain significance | not specified | 2022-10-03 | no assertion criteria provided | clinical testing | DNA sequence analysis of the IL17RD gene demonstrated a sequence change, c.572C>T, in exon 6 that results in an amino acid change, p.Pro191Leu. This sequence change has been previously described in a female individual with normosmic isolated hypogonadotropic hypogonadism (PMID: 32389901). This sequence change has been described in the gnomAD database with a frequency of 0.15% in the East Asian subpopulation (dbSNP rs200088377). The p.Pro191Leu change affects a highly conserved amino acid residue located in a domain of the IL17RD protein that is not known to be functional. In-silico pathogenicity prediction tools (SIFT, PolyPhen2, Align GVGD, REVEL) provide contradictory results for the p.Pro191Leu substitution. Due to insufficient evidences and the lack of functional studies, the clinical significance of the p.Pro191Leu change remains unknown at this time. |