Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001348439 | SCV001542743 | likely benign | Adams-Oliver syndrome 5 | 2023-06-14 | criteria provided, single submitter | clinical testing | |
Women's Health and Genetics/Laboratory Corporation of America, |
RCV003987844 | SCV004803615 | uncertain significance | not specified | 2024-01-22 | criteria provided, single submitter | clinical testing | Variant summary: NOTCH1 c.2835C>G (p.Asp945Glu) results in a conservative amino acid change located in the EGF-like domain (IPR000742) of the encoded protein sequence. Four of five in-silico tools predict a damaging effect of the variant on protein function. The variant allele was found at a frequency of 1.6e-05 in 248774 control chromosomes. The available data on variant occurrences in the general population are insufficient to allow any conclusion about variant significance. To our knowledge, no occurrence of c.2835C>G in individuals affected with Adams-Oliver Syndrome 5 and no experimental evidence demonstrating its impact on protein function have been reported. ClinVar contains an entry for this variant (Variation ID: 1044217). Based on the evidence outlined above, the variant was classified as uncertain significance. |
Ambry Genetics | RCV004651604 | SCV005142241 | uncertain significance | Familial thoracic aortic aneurysm and aortic dissection | 2024-04-17 | criteria provided, single submitter | clinical testing | The c.2835C>G (p.D945E) alteration is located in exon 18 (coding exon 18) of the NOTCH1 gene. This alteration results from a C to G substitution at nucleotide position 2835, causing the aspartic acid (D) at amino acid position 945 to be replaced by a glutamic acid (E). Based on insufficient or conflicting evidence, the clinical significance of this alteration remains unclear. |