Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Center for Human Genetics, |
RCV000660179 | SCV000782173 | likely benign | Connective tissue disorder | 2016-11-01 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV001861714 | SCV002279636 | uncertain significance | Adams-Oliver syndrome 5 | 2022-03-14 | criteria provided, single submitter | clinical testing | In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. Experimental studies and prediction algorithms are not available or were not evaluated, and the functional significance of this variant is currently unknown. This variant has not been reported in the literature in individuals affected with NOTCH1-related conditions. This variant is present in population databases (rs762336270, gnomAD 0.006%). This variant, c.7244_7246dup, results in the insertion of 1 amino acid(s) of the NOTCH1 protein (p.Pro2415dup), but otherwise preserves the integrity of the reading frame. |