Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV002928121 | SCV003262507 | likely benign | not provided | 2022-10-07 | criteria provided, single submitter | clinical testing | |
Neuberg Centre For Genomic Medicine, |
RCV003340563 | SCV004047248 | uncertain significance | Mitochondrial complex III deficiency nuclear type 2 | criteria provided, single submitter | clinical testing | The missense variant in c.906G>A (p.Met302Ile) in TTC19 gene has not been reported previously as a pathogenic variant nor as a benign variant, to our knowledge. This variant is reported with allele frequency of 0.02% in gnomAD database. The amino acid Met at position 302 is changed to a Ile changing protein sequence and it might alter its composition and physico-chemical properties. The amino acid change p.Met302Ile in TTC19 is predicted as conserved by GERP++ and PhyloP across 100 vertebrates. For these reasons, this variant has been classified as Uncertain Significance (VUS). |