Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Eurofins Ntd Llc |
RCV000731433 | SCV000859251 | uncertain significance | not provided | 2018-01-22 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV002536463 | SCV003478247 | uncertain significance | Familial aplasia of the vermis; Meckel-Gruber syndrome | 2022-04-12 | criteria provided, single submitter | clinical testing | In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. Advanced modeling of protein sequence and biophysical properties (such as structural, functional, and spatial information, amino acid conservation, physicochemical variation, residue mobility, and thermodynamic stability) performed at Invitae indicates that this missense variant is not expected to disrupt MKS1 protein function. ClinVar contains an entry for this variant (Variation ID: 595787). This variant has not been reported in the literature in individuals affected with MKS1-related conditions. This variant is not present in population databases (gnomAD no frequency). This sequence change replaces glutamic acid, which is acidic and polar, with aspartic acid, which is acidic and polar, at codon 12 of the MKS1 protein (p.Glu12Asp). |
Fulgent Genetics, |
RCV005027911 | SCV005649667 | uncertain significance | Bardet-Biedl syndrome 13; Meckel syndrome, type 1; Joubert syndrome 28 | 2024-05-07 | criteria provided, single submitter | clinical testing | |
Prevention |
RCV004527764 | SCV004110750 | uncertain significance | MKS1-related disorder | 2024-05-23 | no assertion criteria provided | clinical testing | The MKS1 c.36G>T variant is predicted to result in the amino acid substitution p.Glu12Asp. To our knowledge, this variant has not been reported in the literature or in a large population database, indicating this variant is rare. At this time, the clinical significance of this variant is uncertain due to the absence of conclusive functional and genetic evidence. |