Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Eurofins Ntd Llc |
RCV000405637 | SCV000331593 | pathogenic | not provided | 2014-02-18 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV002514946 | SCV003240539 | pathogenic | CHARGE syndrome | 2022-09-21 | criteria provided, single submitter | clinical testing | This variant is not present in population databases (gnomAD no frequency). This sequence change creates a premature translational stop signal (p.Gln364*) in the CHD7 gene. It is expected to result in an absent or disrupted protein product. Loss-of-function variants in CHD7 are known to be pathogenic (PMID: 22461308, 25077900). This variant has not been reported in the literature in individuals affected with CHD7-related conditions. For these reasons, this variant has been classified as Pathogenic. ClinVar contains an entry for this variant (Variation ID: 166857). |
Prevention |
RCV003398801 | SCV004103703 | pathogenic | CHD7-related disorder | 2024-02-10 | no assertion criteria provided | clinical testing | The CHD7 c.1090C>T variant is predicted to result in premature protein termination (p.Gln364*). To our knowledge, this variant has not been reported in the literature or in a large population database (http://gnomad.broadinstitute.org), indicating this variant is rare. Nonsense variants in CHD7 are expected to be pathogenic. This variant is interpreted as pathogenic. |