Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV000445135 | SCV000520954 | pathogenic | not provided | 2024-02-25 | criteria provided, single submitter | clinical testing | Not observed at significant frequency in large population cohorts (gnomAD); In silico analysis supports that this missense variant has a deleterious effect on protein structure/function; In silico analysis suggests this variant may impact gene splicing; in the absence of RNA/functional studies the actual effect of this sequence change is unknown; This variant is associated with the following publications: (PMID: 22539353, 21554267) |
Ambry Genetics | RCV001266874 | SCV001445054 | likely pathogenic | Inborn genetic diseases | 2017-12-05 | criteria provided, single submitter | clinical testing |