Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Prevention |
RCV003400427 | SCV004103950 | likely pathogenic | CHD7-related disorder | 2023-09-28 | criteria provided, single submitter | clinical testing | The CHD7 c.3149_3156delinsGTC variant is predicted to result in a frameshift and premature protein termination (p.Gln1050Argfs*9). To our knowledge, this variant has not been reported in the literature or in a large population database (http://gnomad.broadinstitute.org), indicating this variant is rare. Frameshift variants in CHD7 are expected to be pathogenic. This variant is interpreted as likely pathogenic. |