Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Institute of Human Genetics, |
RCV001293772 | SCV001482420 | pathogenic | CHARGE syndrome | 2021-03-03 | criteria provided, single submitter | clinical testing | This splice variant was found in a patient with clinically verified CHARGE syndrome. The mutation affects the canonical splice site and other mutations affecting this splice site were already described to be pathogenic (Janssen et al. 2012). In summary, using ACMG criteria PVS1_vstr, PM2, PP5 we classified this variant as pathogenic |