Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Prevention |
RCV003926816 | SCV004745710 | pathogenic | CHD7-related disorder | 2023-10-27 | no assertion criteria provided | clinical testing | The CHD7 c.5665+1G>A variant is predicted to disrupt the GT donor site and interfere with normal splicing. To our knowledge, this variant has not been reported in the literature or in a large population database (http://gnomad.broadinstitute.org), indicating this variant is rare. Another variant at the same nucleotide has been reported in at least two individuals with intellectual disability and/or CHARGE syndrome (Table S3, Grozeva et al. 2015. PubMed ID: 26350204; Villate et al. 2018. PubMed ID: 29434620). Variants that disrupt the consensus splice donor site in CHD7 are expected to be pathogenic. This variant is interpreted as pathogenic. |