Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV000482952 | SCV000567489 | pathogenic | not provided | 2015-07-29 | criteria provided, single submitter | clinical testing | The c.7297delG deletion in the CHD7 gene causes a frameshift starting with codon Valine 2433, changesthis amino acid to a Serine residue and creates a premature Stop codon at position 10 of the new readingframe, denoted p.Val2433SerfsX10. This variant is predicted to cause loss of normal protein functioneither through protein truncation or nonsense-mediated mRNA decay. Although this deletion has not beenpreviously reported to our knowledge, we consider it to be a pathogenic variant. |
Institute of Human Genetics, |
RCV001253666 | SCV001429504 | pathogenic | CHARGE syndrome | 2017-11-08 | criteria provided, single submitter | clinical testing |